CWF19L1

Chr 10AR

CWF19 like cell cycle control factor 1

Also known as: C19L1, SCAR17, hDrn1

The protein is a member of the CWF19 family involved in pre-mRNA splicing. Mutations cause autosomal recessive spinocerebellar ataxia type 17, characterized by cerebellar ataxia and mild cognitive disability. This gene shows extreme intolerance to loss-of-function variants (pLI ~1.0), indicating it is highly constrained and essential for normal function.

OMIMResearchSummary from RefSeq, OMIM
ARLOEUF 1.151 OMIM phenotype
Clinical SummaryCWF19L1
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Gene-Disease Validity (ClinGen)
autosomal recessive cerebellar ataxia · ARDefinitive

Definitive — sufficient evidence for diagnostic panels

Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.15LOEUF
pLI 0.000
Z-score 0.89
OE 0.83 (0.611.15)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
1.10Z-score
OE missense 0.82 (0.730.91)
232 obs / 283.9 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.83 (0.611.15)
00.351.4
Missense OE0.82 (0.730.91)
00.61.4
Synonymous OE0.87
01.21.6
LoF obs/exp: 26 / 31.4Missense obs/exp: 232 / 283.9Syn Z: 1.01

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CWF19L1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Full-Text Mentions
NLP-detected gene mentions in article bodies · via PubTator3
PubTator3
Top 5 full-text resultsSearch PubTator3 ↗