CTD-2154B17.1

Chr 5AR

uncharacterized CTD-2154B17.1

Primary Disease Associations & Inheritance

Congenital cataracts, facial dysmorphism, and neuropathyMIM #604168
AR
43
ClinVar variants
41
Pathogenic / LP
pLI score
0
Active trials
Clinical SummaryCTD-2154B17.1
📋
ClinVar Variants
41 Pathogenic / Likely Pathogenic· 2 VUS of 43 total submissions
Some data sources returned errors (1)

ensembl: Error: Ensembl fetch failed: 400 for https://rest.ensembl.org/lookup/symbol/homo_sapiens/CTD-2154B17.1?content-type=application/json&expand=1

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

43 submitted variants in ClinVar

Classification Summary

Pathogenic41
VUS2
41
Pathogenic
2
VUS

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories· variant type breakdown unavailable

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
41
Likely Pathogenic
0
VUS
2
Likely Benign
0
Benign
0
Total43

Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

CTD-2154B17.1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

OMIM — Genotype-Phenotype Relationships

3 OMIM entries