CTC1

Chr 17AR

CST telomere replication complex component 1

Also known as: AAF-132, AAF132, C17orf68, CRMCC, tmp494178

The protein is a component of the CST complex that protects telomeres from degradation and promotes DNA replication under stress conditions, including telomere replication and recovery from DNA damage. Autosomal recessive mutations cause cerebroretinal microangiopathy with calcifications and cysts, a disorder affecting the brain and retinal vasculature. The gene shows low constraint against loss-of-function variants (pLI near zero), consistent with its recessive inheritance pattern.

GeneReviewsOMIMResearchSummary from RefSeq, OMIM, UniProt
LOFmechanismARLOEUF 0.631 OMIM phenotype
Clinical SummaryCTC1
🧬
Gene-Disease Validity (ClinGen)
cerebroretinal microangiopathy with calcifications and cysts 1 · ARDefinitive

Definitive — sufficient evidence for diagnostic panels

Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📖
GeneReview available — CTC1
Authoritative clinical overview · Recommended first read
Open GeneReview ↗

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.63LOEUF
pLI 0.000
Z-score 3.97
OE 0.46 (0.340.63)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
0.50Z-score
OE missense 0.95 (0.891.01)
645 obs / 682.0 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.46 (0.340.63)
00.351.4
Missense OE0.95 (0.891.01)
00.61.4
Synonymous OE1.00
01.21.6
LoF obs/exp: 29 / 63.0Missense obs/exp: 645 / 682.0Syn Z: -0.04

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CTC1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →