The cystatin superfamily encompasses proteins that contain multiple cystatin-like sequences. Some of the members are active cysteine protease inhibitors, while others have lost or perhaps never acquired this inhibitory activity. There are three inhibitory families in the superfamily, including the type 1 cystatins (stefins), type 2 cystatins and the kininogens. The type 2 cystatin proteins are a class of cysteine proteinase inhibitors found in a variety of human fluids and secretions, where they appear to provide protective functions. The cystatin locus on chromosome 20 contains the majority of the type 2 cystatin genes and pseudogenes. This gene is located in the cystatin locus and encodes a cysteine proteinase inhibitor found in saliva, tears, urine, and seminal fluid. [provided by RefSeq, Jul 2008]

ResearchGenerating clinical summary…
0
Active trials
36
Pubs (1 yr)
P/LP submissions
P/LP missense
1.96
LOEUF
DN
Mechanism· predicted
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.96LOEUF
pLI 0.000
Z-score -1.79
OE 1.88 (1.001.96)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
-2.20Z-score
OE missense 1.68 (1.461.91)
141 obs / 84.1 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?1.88 (1.001.96)
00.351.4
Missense OE?1.68 (1.461.91)
00.61.4
Synonymous OE?1.75
01.21.6
LoF obs/exp: 9 / 4.8Missense obs/exp: 141 / 84.1Syn Z: -3.52

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CST1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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