CSRNP3

Chr 2

cysteine and serine rich nuclear protein 3

Also known as: FAM130A2, MBU1, PPP1R73, TAIP-2, TAIP2

CSRNP3 encodes a transcriptional activator that binds specific DNA sequences and promotes apoptosis. Mutations cause autosomal recessive neurodevelopmental disorders with intellectual disability, seizures, and brain malformations. The gene shows high constraint against loss-of-function variants (LOEUF 0.445), indicating intolerance to inactivating mutations.

OMIMResearchSummary from RefSeq, UniProt
LOEUF 0.45
Clinical SummaryCSRNP3
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.50) — some intolerance to loss-of-function variants.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.45LOEUF
pLI 0.500
Z-score 3.55
OE 0.21 (0.110.45)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
1.59Z-score
OE missense 0.75 (0.680.84)
248 obs / 329.1 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.21 (0.110.45)
00.351.4
Missense OE0.75 (0.680.84)
00.61.4
Synonymous OE1.03
01.21.6
LoF obs/exp: 5 / 23.6Missense obs/exp: 248 / 329.1Syn Z: -0.23

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CSRNP3 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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