CRMP1

Chr 4

collapsin response mediator protein 1

Also known as: CRMP-1, DPYSL1, DRP-1, DRP1, ULIP-3

The protein mediates semaphorin signaling that controls axon guidance during neural development by promoting cytoskeletal remodeling and growth cone collapse. Mutations cause autosomal dominant developmental delay, intellectual disability, and seizures with onset in infancy or early childhood. The gene is highly constrained against loss-of-function variants (pLI = 0.99, LOEUF = 0.28), reflecting its essential role in nervous system development.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
8
Pubs (1 yr)
90
P/LP submissions
0%
P/LP missense
0.28
LOEUF· LoF intol.
Mechanism
Clinical SummaryCRMP1
Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 0.99). One damaged copy is likely sufficient to cause disease.
📋
ClinVar Variants
90 unique Pathogenic / Likely Pathogenic· 113 VUS of 227 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint
0.28LOEUF
pLI 0.992
Z-score 4.34
OE 0.11 (0.050.28)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint
2.41Z-score
OE missense 0.65 (0.580.72)
244 obs / 375.6 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios
LoF OE0.11 (0.050.28)
00.351.4
Missense OE0.65 (0.580.72)
00.61.4
Synonymous OE1.08
01.21.6
LoF obs/exp: 3 / 27.6Missense obs/exp: 244 / 375.6Syn Z: -0.82

ClinVar Variant Classifications

227 submitted variants in ClinVar

Classification Summary

Pathogenic85
Likely Pathogenic5
VUS113
Likely Benign6
Benign9
Conflicting1
85
Pathogenic
5
Likely Pathogenic
113
VUS
6
Likely Benign
9
Benign
1
Conflicting

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
85
0
85
Likely Pathogenic
1
0
4
0
5
VUS
1
104
8
0
113
Likely Benign
0
0
0
6
6
Benign
0
1
2
6
9
Conflicting
1
Total21059912219

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

CRMP1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →