CRELD1

Chr 3

CRELD disulfide isomerase 1

Also known as: AVSD2, CIRRIN, JELANS

This gene encodes a member of a subfamily of epidermal growth factor-related proteins. The encoded protein is characterized by a cysteine-rich with epidermal growth factor-like domain. This protein may function as a cell adhesion molecule. Mutations in this gene are the cause of atrioventricular septal defect. Alternate splicing results in multiple transcript variants.[provided by RefSeq, Apr 2010]

ResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtAtrioventricular septal defect 2
UniProtJeffries-Lakhani neurodevelopmental syndrome

Clinical highlights

Gene-disease validity (ClinGen)
congenital heart disease · ADLimitednot for standalone diagnostic reporting
1
Active trials
5
Pubs (1 yr)
P/LP submissions
P/LP missense
1.05
LOEUF
Multiple*
Mechanism· predicted
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.05LOEUF
pLI 0.000
Z-score 1.36
OE 0.73 (0.521.05)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
0.17Z-score
OE missense 0.97 (0.871.08)
235 obs / 242.7 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.73 (0.521.05)
00.351.4
Missense OE?0.97 (0.871.08)
00.61.4
Synonymous OE?1.20
01.21.6
LoF obs/exp: 21 / 28.9Missense obs/exp: 235 / 242.7Syn Z: -1.48

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CRELD1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.