CPSF1

Chr 8

cleavage and polyadenylation specific factor 1

Component of the cleavage and polyadenylation specificity factor (CPSF) complex that plays a key role in pre-mRNA 3'-end formation, recognizing the AAUAAA signal sequence and interacting with poly(A) polymerase and other factors to bring about cleavage and poly(A) addition. This subunit is involved in the RNA recognition step of the polyadenylation reaction (PubMed:14749727). May play a role in eye morphogenesis and the development of retinal ganglion cell projections to the midbrain (By similarity)

ResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtMyopia 27, autosomal dominant
0
Active trials
12
Pubs (1 yr)
P/LP submissions
P/LP missense
0.54
LOEUF
LOF
Mechanism· predicted
Some data sources returned errors (2)

ncbi: Error: NCBI fetch failed: 429 https://eutils.ncbi.nlm.nih.gov/entrez/eutils/esearch.fcgi

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint?
0.54LOEUF
pLI 0.000
Z-score 4.84
OE 0.40 (0.300.54)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint?
2.80Z-score
OE missense 0.75 (0.700.79)
719 obs / 963.5 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios?
LoF OE?0.40 (0.300.54)
00.351.4
Missense OE?0.75 (0.700.79)
00.61.4
Synonymous OE?1.19
01.21.6
LoF obs/exp: 30 / 75.3Missense obs/exp: 719 / 963.5Syn Z: -3.05

ClinVar

No ClinVar data available.

Protein Context — Lollipop Plot

CPSF1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →