CORO7

Chr 16

coronin 7

Also known as: 0610011B16Rik, CRN7, POD1

The protein regulates F-actin to facilitate anterograde transport from the Golgi apparatus to endosomes and helps maintain Golgi morphology. Mutations cause autosomal recessive developmental delay, intellectual disability, seizures, and microcephaly with onset in infancy or early childhood. The gene shows extremely low constraint against loss-of-function variants, which is consistent with the recessive inheritance pattern observed clinically.

ResearchSummary from RefSeq, UniProt
LOEUF 1.02
Clinical SummaryCORO7
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
33 unique Pathogenic / Likely Pathogenic· 174 VUS of 228 total submissions
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.02LOEUF
pLI 0.000
Z-score 1.44
OE 0.79 (0.621.02)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.19Z-score
OE missense 1.02 (0.951.09)
593 obs / 579.8 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.79 (0.621.02)
00.351.4
Missense OE1.02 (0.951.09)
00.61.4
Synonymous OE1.08
01.21.6
LoF obs/exp: 45 / 56.7Missense obs/exp: 593 / 579.8Syn Z: -1.07

ClinVar Variant Classifications

228 submitted variants in ClinVar

Classification Summary

Pathogenic33
VUS174
Likely Benign14
Benign4
33
Pathogenic
174
VUS
14
Likely Benign
4
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
33
0
33
Likely Pathogenic
0
0
0
0
0
VUS
0
163
11
0
174
Likely Benign
0
13
0
1
14
Benign
0
2
0
2
4
Total0178443225

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

CORO7 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC