COG2

Chr 1

component of oligomeric golgi complex 2

Also known as: CDG2Q, LDLC

This gene encodes a subunit of the conserved oligomeric Golgi complex that is required for maintaining normal structure and activity of the Golgi complex. The encoded protein specifically interacts with the USO1 vesicle docking protein and may be necessary for normal Golgi ribbon formation and trafficking of Golgi enzymes. Mutations of this gene are associated with abnormal glycosylation within the Golgi apparatus. Alternative splicing results in multiple transcript variants.[provided by RefSeq, Feb 2009]

ResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtCongenital disorder of glycosylation 2Q

Clinical highlights

Gene-disease validity (ClinGen)
congenital disorder of glycosylation, type IIq · ARLimitednot for standalone diagnostic reporting
0
Active trials
3
Pubs (1 yr)
P/LP submissions
P/LP missense
0.59
LOEUF
DN
Mechanism· predicted
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint?
0.59LOEUF
pLI 0.000
Z-score 3.63
OE 0.39 (0.260.59)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint?
0.85Z-score
OE missense 0.88 (0.810.96)
351 obs / 399.0 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.39 (0.260.59)
00.351.4
Missense OE?0.88 (0.810.96)
00.61.4
Synonymous OE?1.11
01.21.6
LoF obs/exp: 16 / 41.1Missense obs/exp: 351 / 399.0Syn Z: -1.04

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

COG2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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