CNTNAP3B

Chr 9

contactin associated protein family member 3B

The protein is predicted to function in cell adhesion and is located in cellular membranes. Mutations in this gene cause neurodevelopmental disorders with intellectual disability, though the clinical phenotype is not well-characterized given limited reported cases. The gene shows very low constraint against loss-of-function variants (high LOEUF score), suggesting it may tolerate some degree of functional disruption.

ResearchSummary from RefSeq
LOEUF 1.67
Clinical SummaryCNTNAP3B
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
3 unique Pathogenic / Likely Pathogenic· 270 VUS of 300 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.67LOEUF
pLI 0.000
Z-score -1.39
OE 1.27 (0.981.67)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-2.48Z-score
OE missense 1.40 (1.291.52)
423 obs / 301.8 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE1.27 (0.981.67)
00.351.4
Missense OE1.40 (1.291.52)
00.61.4
Synonymous OE1.28
01.21.6
LoF obs/exp: 38 / 29.8Missense obs/exp: 423 / 301.8Syn Z: -2.49

ClinVar Variant Classifications

300 submitted variants in ClinVar

Classification Summary

Pathogenic2
Likely Pathogenic1
VUS270
Likely Benign24
2
Pathogenic
1
Likely Pathogenic
270
VUS
24
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
2
0
2
Likely Pathogenic
0
0
1
0
1
VUS
0
270
0
0
270
Likely Benign
0
16
2
6
24
Benign
0
0
0
0
0
Total028656297

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

CNTNAP3B · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
Open Research Assistant →
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found