CNTN1

Chr 12AR

contactin 1

Also known as: CMYO12, CMYP12, F3, GP135, MYPCN

This gene encodes contactin-1, a GPI-anchored neuronal membrane protein that mediates cell surface interactions during nervous system development and participates in the formation of paranodal axo-glial junctions in myelinated peripheral nerves. Mutations cause congenital myopathy 12, which follows an autosomal recessive inheritance pattern. The gene is highly constrained against loss-of-function variants (LOEUF 0.373), reflecting its critical role in nervous system function.

OMIMResearchSummary from RefSeq, OMIM, UniProt
DNmechanismARLOEUF 0.371 OMIM phenotype
Clinical SummaryCNTN1
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.24) despite low pLI — interpret in context.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.37LOEUF
pLI 0.151
Z-score 5.40
OE 0.24 (0.160.37)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
2.05Z-score
OE missense 0.76 (0.700.82)
418 obs / 553.5 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios
LoF OE0.24 (0.160.37)
00.351.4
Missense OE0.76 (0.700.82)
00.61.4
Synonymous OE1.03
01.21.6
LoF obs/exp: 14 / 58.7Missense obs/exp: 418 / 553.5Syn Z: -0.37
DN
0.6938th %ile
GOF
0.6248th %ile
LOF
0.3842th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CNTN1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
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Key Publications
Landmark & review papers · by relevance
PubMed
Top 5 results · since 2015Search PubMed ↗