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CNE5

Chr X, YADAR

CNE5 enhancer downstream of SHOX

CNE5 is a conserved non-coding enhancer element that regulates SHOX gene expression in bone and limb development. Deletions and duplications of this region cause Leri-Weill dyschondrosteosis, idiopathic short stature, and Langer mesomelic dysplasia, affecting skeletal growth and limb proportions. CNE5 is located in the pseudoautosomal region of the X and Y chromosomes and shows pseudoautosomal inheritance patterns.

OMIMResearchSummary from RefSeq, OMIM
AD/AR7 OMIM phenotypes
Clinical SummaryCNE5
📋
ClinVar Variants
34 unique Pathogenic / Likely Pathogenic· 2 VUS of 36 total submissions
Some data sources returned errors (2)

ensembl: Error: Ensembl fetch failed: 400 for https://rest.ensembl.org/lookup/symbol/homo_sapiens/CNE5?content-type=application/json&expand=1

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

36 submitted variants in ClinVar

Classification Summary

Pathogenic34
VUS2
34
Pathogenic
2
VUS

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories· variant type breakdown unavailable

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
34
Likely Pathogenic
0
VUS
2
Likely Benign
0
Benign
0
Total36

Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

CNE5 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
RARE DOSAGE ABNORMALITIES - COPY NUMBER VARIATIONS FLANKING THE SHOX GENE.
Gherlan I et al.·Acta Endocrinol (Buchar)
2023Case report
Top 1 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found