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CNE-3

Chr X, YARAD

CNE-3 enhancer upstream of SHOX

CNE-3 is a conserved genomic enhancer element located in the pseudoautosomal region that regulates SHOX gene expression through chromatin looping interactions. Mutations including deletions and duplications of this regulatory region cause Leri-Weill dyschondrosteosis and idiopathic short stature, with additional associations reported in autism spectrum disorders and neurodevelopmental conditions. The inheritance pattern varies depending on the specific mutation and associated phenotype.

OMIMResearchSummary from RefSeq, OMIM
AR/AD5 OMIM phenotypes
Clinical SummaryCNE-3
📋
ClinVar Variants
30 unique Pathogenic / Likely Pathogenic· 2 VUS of 34 total submissions
Some data sources returned errors (2)

ensembl: Error: Ensembl fetch failed: 400 for https://rest.ensembl.org/lookup/symbol/homo_sapiens/CNE-3?content-type=application/json&expand=1

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

34 submitted variants in ClinVar

Classification Summary

Pathogenic30
VUS2
Benign2
30
Pathogenic
2
VUS
2
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories· variant type breakdown unavailable

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
30
Likely Pathogenic
0
VUS
2
Likely Benign
0
Benign
2
Total34

Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

CNE-3 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 1 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC