CMTM1

Chr 16

CKLF like MARVEL transmembrane domain containing 1

Also known as: CKLFH, CKLFH1, CKLFSF1

The protein encoded by this gene belongs to the chemokine-like factor superfamily and contributes to testicular development. Mutations in CMTM1 cause disease through a predicted gain-of-function mechanism, though the specific associated neurological phenotype and inheritance pattern are not established in the available data.

Summary from RefSeq, Mechanism
Research Assistant →
0
Active trials
4
Pubs (1 yr)
0
P/LP submissions
P/LP missense
1.31
LOEUF
Multiple*
Mechanism· predicted
Clinical SummaryCMTM1
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.31LOEUF
pLI 0.002
Z-score 0.97
OE 0.63 (0.331.31)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.42Z-score
OE missense 0.91 (0.801.04)
168 obs / 184.2 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.63 (0.331.31)
00.351.4
Missense OE0.91 (0.801.04)
00.61.4
Synonymous OE0.94
01.21.6
LoF obs/exp: 5 / 8.0Missense obs/exp: 168 / 184.2Syn Z: 0.45
DN
0.81top 10%
GOF
0.88top 5%
LOF
0.1598th %ile

This gene has evidence for multiple mechanisms of pathogenicity (gain-of-function and dominant-negative). Both the Badonyi & Marsh prediction and the broader genomic evidence point to gain-of-function as the predominant mechanism. Different variants in this gene may act through different mechanisms — interpret in context of the specific variant.

GOFprediction above median
DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CMTM1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC