CLEC19A

Chr 16

C-type lectin domain containing 19A

The protein is predicted to bind carbohydrates and localize to the extracellular region. Mutations in this gene have been associated with neurodevelopmental disorders, though the clinical phenotype and inheritance pattern are not well-established based on current data. The gene shows relatively low constraint to loss-of-function variation.

ResearchSummary from RefSeq
MultiplemechanismLOEUF 1.60
Clinical SummaryCLEC19A
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.60LOEUF
pLI 0.004
Z-score 0.56
OE 0.74 (0.361.60)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.81Z-score
OE missense 0.73 (0.580.92)
51 obs / 70.2 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.74 (0.361.60)
00.351.4
Missense OE0.73 (0.580.92)
00.61.4
Synonymous OE0.85
01.21.6
LoF obs/exp: 4 / 5.4Missense obs/exp: 51 / 70.2Syn Z: 0.63
DN
0.7229th %ile
GOF
0.7029th %ile
LOF
0.2583th %ile

This gene has evidence for multiple mechanisms of pathogenicity (dominant-negative and gain-of-function). Both the Badonyi & Marsh prediction and the broader genomic evidence point to dominant-negative as the predominant mechanism. Different variants in this gene may act through different mechanisms — interpret in context of the specific variant.

DNprediction above median
GOFprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CLEC19A · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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