CIDEC

Chr 3AR

cell death inducing DFFA like effector c

Also known as: CIDE-3, CIDE3, FPLD5, FSP27

The CIDEC protein is a lipid transferase expressed in white adipose tissue that promotes lipid droplet fusion and enlargement, restricting lipolysis and favoring lipid storage. Mutations cause familial partial lipodystrophy type 5, inherited in an autosomal recessive pattern. The gene shows low constraint to loss-of-function variation (pLI = 0.009, LOEUF = 0.943), consistent with recessive inheritance.

OMIMResearchSummary from RefSeq, OMIM, UniProt
DNmechanismARLOEUF 0.941 OMIM phenotype
Clinical SummaryCIDEC
Population Constraint (gnomAD)
Low constraint (pLI 0.01) — loss-of-function variants are relatively tolerated in the population.
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Clinical Trials
1 active or recruiting trial — potential therapeutic options may be available

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.94LOEUF
pLI 0.009
Z-score 1.71
OE 0.45 (0.230.94)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
-0.67Z-score
OE missense 1.16 (1.021.32)
163 obs / 140.7 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.45 (0.230.94)
00.351.4
Missense OE1.16 (1.021.32)
00.61.4
Synonymous OE1.17
01.21.6
LoF obs/exp: 5 / 11.2Missense obs/exp: 163 / 140.7Syn Z: -1.02
DN
0.7229th %ile
GOF
0.6149th %ile
LOF
0.3552th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CIDEC · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold
Clinical Literature
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