CHRND

Chr 2

cholinergic receptor nicotinic delta subunit

Also known as: ACHRD, CMS2A, CMS3A, CMS3B, CMS3C, FCCMS, SCCMS

The acetylcholine receptor of muscle has 5 subunits of 4 different types: 2 alpha and 1 each of beta, gamma and delta subunits. After acetylcholine binding, the receptor undergoes an extensive conformation change that affects all subunits and leads to opening of an ion-conducting channel across the plasma membrane. Defects in this gene are a cause of multiple pterygium syndrome lethal type (MUPSL), congenital myasthenic syndrome slow-channel type (SCCMS), and congenital myasthenic syndrome fast-channel type (FCCMS). Several transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Jul 2015]

GeneReviewsResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtMultiple pterygium syndrome, lethal type
UniProtMyasthenic syndrome, congenital, 3A, slow-channel
UniProtMyasthenic syndrome, congenital, 3B, fast-channel
UniProtMyasthenic syndrome, congenital, 3C, associated with acetylcholine receptor deficiency
0
Active trials
14
Pubs (1 yr)
P/LP submissions
P/LP missense
0.98
LOEUF
Multiple*
Mechanism· predicted
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GeneReview available — CHRND
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Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.98LOEUF
pLI 0.000
Z-score 1.65
OE 0.65 (0.450.98)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
0.05Z-score
OE missense 0.99 (0.901.09)
296 obs / 298.6 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.65 (0.450.98)
00.351.4
Missense OE?0.99 (0.901.09)
00.61.4
Synonymous OE?1.01
01.21.6
LoF obs/exp: 17 / 26.1Missense obs/exp: 296 / 298.6Syn Z: -0.06

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CHRND · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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