CFAP96

Chr 4

cilia and flagella associated protein 96

Also known as: C4orf47

The protein localizes to non-motile cilia, centrosomes, and cytoplasmic microtubules where it likely functions in ciliary structure or signaling. Mutations cause autosomal recessive retinal dystrophy and Bardet-Biedl syndrome, ciliopathies that can present with vision loss, obesity, kidney dysfunction, and developmental delays. The gene shows minimal constraint against loss-of-function variants, consistent with recessive inheritance where one functional copy is insufficient.

Summary from RefSeq
Research Assistant →
0
Active trials
0
Pubs (1 yr)
117
P/LP submissions
0%
P/LP missense
1.02
LOEUF
Mechanism
Clinical SummaryCFAP96
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
116 unique Pathogenic / Likely Pathogenic· 69 VUS of 218 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.02LOEUF
pLI 0.001
Z-score 1.53
OE 0.54 (0.311.02)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
1.23Z-score
OE missense 0.71 (0.600.84)
101 obs / 142.5 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.54 (0.311.02)
00.351.4
Missense OE0.71 (0.600.84)
00.61.4
Synonymous OE1.00
01.21.6
LoF obs/exp: 7 / 12.9Missense obs/exp: 101 / 142.5Syn Z: 0.02

ClinVar Variant Classifications

218 submitted variants in ClinVar

Classification Summary

Pathogenic104
Likely Pathogenic12
VUS69
Likely Benign10
Benign6
Conflicting1
104
Pathogenic
12
Likely Pathogenic
69
VUS
10
Likely Benign
6
Benign
1
Conflicting

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
1
0
103
0
104
Likely Pathogenic
1
0
11
0
12
VUS
1
46
22
0
69
Likely Benign
1
2
5
2
10
Benign
0
1
2
3
6
Conflicting
1
Total4491435202

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

CFAP96 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
Open Research Assistant →
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found