CFAP53

Chr 18

cilia and flagella associated protein 53

Also known as: CCDC11, HTX6

This gene belongs to the CFAP53 family. It was found to be differentially expressed by the ciliated cells of frog epidermis and in skin fibroblasts from human. Mutations in this gene are associated with visceral heterotaxy-6, which implicates this gene in determination of left-right asymmetric patterning. [provided by RefSeq, Aug 2015]

ResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtHeterotaxy, visceral, 6, autosomal
0
Active trials
5
Pubs (1 yr)
P/LP submissions
P/LP missense
1.34
LOEUF
Multiple*
Mechanism· predicted
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.34LOEUF
pLI 0.000
Z-score 0.10
OE 0.98 (0.721.34)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
-0.58Z-score
OE missense 1.10 (1.001.21)
300 obs / 273.1 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?0.98 (0.721.34)
00.351.4
Missense OE?1.10 (1.001.21)
00.61.4
Synonymous OE?1.10
01.21.6
LoF obs/exp: 28 / 28.6Missense obs/exp: 300 / 273.1Syn Z: -0.75

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CFAP53 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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