CFAP52

Chr 17AR

cilia and flagella associated protein 52

Also known as: HTX10, WDR16, WDRPUH

The protein is a microtubule inner protein that is part of dynein-decorated doublet microtubules in cilia axoneme and is important for proper ciliary and flagellar beating. Mutations cause autosomal recessive heterotaxy with visceral organ malposition and male infertility due to defective sperm flagellar function. This gene shows low constraint against loss-of-function variants (LOEUF 1.242), affecting both embryonic left-right patterning through motile cilia dysfunction and reproductive function.

OMIMResearchSummary from RefSeq, OMIM, UniProt
ARLOEUF 1.241 OMIM phenotype
Clinical SummaryCFAP52
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.24LOEUF
pLI 0.000
Z-score 0.48
OE 0.91 (0.671.24)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.18Z-score
OE missense 0.97 (0.891.06)
355 obs / 364.6 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.91 (0.671.24)
00.351.4
Missense OE0.97 (0.891.06)
00.61.4
Synonymous OE0.96
01.21.6
LoF obs/exp: 28 / 30.9Missense obs/exp: 355 / 364.6Syn Z: 0.33

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CFAP52 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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