CFAP418

Chr 8AR

cilia and flagella associated protein 418

Also known as: BBS21, C8orf37, CORD16, FAP418, MOT25, RP64, smalltalk

The encoded protein localizes to the base of primary cilia and may be involved in photoreceptor outer segment disk morphogenesis. Mutations cause autosomal recessive retinal dystrophies including cone-rod dystrophy, retinitis pigmentosa, and Bardet-Biedl syndrome. This gene follows autosomal recessive inheritance and shows low constraint against loss-of-function variants (pLI <0.01, LOEUF 1.42).

Summary from RefSeq, OMIM, UniProt
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Primary Disease Associations & Inheritance

Bardet-Biedl syndrome 21MIM #617406
AR
Cone-rod dystrophy 16MIM #614500
AR
Retinitis pigmentosa 64MIM #614500
AR
0
Active trials
2
Pubs (1 yr)
0
P/LP submissions
P/LP missense
1.42
LOEUF
LOF
Mechanism· G2P
Clinical SummaryCFAP418
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Gene-Disease Validity (ClinGen)
ciliopathy · ARDefinitive

Definitive — sufficient evidence for diagnostic panels

Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.42LOEUF
pLI 0.000
Z-score 0.61
OE 0.79 (0.461.42)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.07Z-score
OE missense 1.02 (0.881.19)
117 obs / 114.8 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.79 (0.461.42)
00.351.4
Missense OE1.02 (0.881.19)
00.61.4
Synonymous OE0.70
01.21.6
LoF obs/exp: 8 / 10.1Missense obs/exp: 117 / 114.8Syn Z: 1.49

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CFAP418 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC