CES1

Chr 16AD

carboxylesterase 1

Also known as: ACAT, CE-1, CEH, CES2, HMSE, HMSE1, PCE-1, REH

This gene encodes a member of the carboxylesterase large family. The family members are responsible for the hydrolysis or transesterification of various xenobiotics, such as cocaine and heroin, and endogenous substrates with ester, thioester, or amide bonds. They may participate in fatty acyl and cholesterol ester metabolism, and may play a role in the blood-brain barrier system. This enzyme is the major liver enzyme and functions in liver drug clearance. Mutations of this gene cause carboxylesterase 1 deficiency. Three transcript variants encoding three different isoforms have been found for this gene. [provided by RefSeq, Jun 2010]

OMIMResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

Drug metabolism, altered, CES1-relatedMIM #618057
AD
2
Active trials
110
Pubs (1 yr)
P/LP submissions
P/LP missense
1.46
LOEUF
DN
Mechanism· predicted

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.46LOEUF
pLI 0.000
Z-score -0.09
OE 1.02 (0.731.46)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
-2.00Z-score
OE missense 1.38 (1.251.51)
307 obs / 223.1 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?1.02 (0.731.46)
00.351.4
Missense OE?1.38 (1.251.51)
00.61.4
Synonymous OE?1.45
01.21.6
LoF obs/exp: 22 / 21.6Missense obs/exp: 307 / 223.1Syn Z: -3.37

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CES1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.