CERS2

Chr 1

ceramide synthase 2

Also known as: L3, LASS2, SP260, TMSG1

This gene encodes a protein that has sequence similarity to yeast longevity assurance gene 1. Mutation or overexpression of the related gene in yeast has been shown to alter yeast lifespan. The human protein may play a role in the regulation of cell growth. Alternatively spliced transcript variants encoding the same protein have been described. [provided by RefSeq, Jul 2008]

ResearchGenerating clinical summary…
LOEUF 0.43
Clinical SummaryCERS2
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.22) despite low pLI — interpret in context.
📋
ClinVar Variants
44 VUS of 67 total submissions
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint?
0.43LOEUF
pLI 0.480
Z-score 3.83
OE 0.22 (0.120.43)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint?
1.76Z-score
OE missense 0.68 (0.590.77)
158 obs / 233.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.22 (0.120.43)
00.351.4
Missense OE?0.68 (0.590.77)
00.61.4
Synonymous OE?1.06
01.21.6
LoF obs/exp: 6 / 27.8Missense obs/exp: 158 / 233.8Syn Z: -0.45

ClinVar Variant Classifications

67 submitted variants in ClinVar

Classification Summary

VUS44
Likely Benign4
Benign3
44
VUS
4
Likely Benign
3
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
0
0
0
Likely Pathogenic
0
0
0
0
0
VUS
0
44
0
0
44
Likely Benign
0
4
0
0
4
Benign
0
0
0
3
3
Total0480351

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

14 pathogenic / likely-pathogenic (of 17) ClinVar copy-number / structural variants overlap CERS2 — these span large chromosomal regions, not the gene specifically, and are excluded from the counts above. Explore in CNV tools →

Protein Context — Lollipop Plot

CERS2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →