CEP152

Chr 15AR

centrosomal protein 152

The protein localizes to the centrosome and functions in centrosome biogenesis and microtubule organization. Mutations cause primary microcephaly (MCPH4) and Seckel syndrome 5 through autosomal recessive inheritance. The pathogenic mechanism involves disrupted centrosome function leading to abnormal cell division and impaired brain development.

OMIMResearchSummary from RefSeq, OMIM, UniProt
LOFmechanismARLOEUF 0.822 OMIM phenotypes
Clinical SummaryCEP152
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Gene-Disease Validity (ClinGen)
microcephaly with or without short stature · ARDefinitive

Definitive — sufficient evidence for diagnostic panels

Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
Some data sources returned errors (1)

ncbi: Error: NCBI fetch failed: 429 https://eutils.ncbi.nlm.nih.gov/entrez/eutils/esearch.fcgi

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.82LOEUF
pLI 0.000
Z-score 2.91
OE 0.66 (0.530.82)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
0.03Z-score
OE missense 1.00 (0.941.06)
831 obs / 833.3 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.66 (0.530.82)
00.351.4
Missense OE1.00 (0.941.06)
00.61.4
Synonymous OE1.02
01.21.6
LoF obs/exp: 56 / 85.0Missense obs/exp: 831 / 833.3Syn Z: -0.33
Curated Mechanism (G2P)Gene2Phenotype (DDG2P) ↗
definitiveCEP152-related developmental disorderLOFAR

Predictions shown for reference only — model trained on dominant genes, not applicable to AR conditions.

DN
0.6550th %ile
GOF
0.5758th %ile
LOF
0.3647th %ile

The Badonyi & Marsh prediction model was trained exclusively on dominant disease genes. Predictions are not reliable for genes with autosomal recessive inheritance and are shown at reduced opacity for reference only.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CEP152 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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