CDR2

Chr 16

cerebellar degeneration related protein 2

Also known as: CDR62, Yo

CDR2 encodes a cytoplasmic protein whose normal function is not well characterized. Mutations cause cerebellar degeneration-related protein 2-associated cerebellar ataxia, a neurodegenerative disorder affecting the cerebellum. The gene shows no intolerance to loss-of-function variants (pLI near 0), and inheritance pattern information is not available from the provided data.

OMIMResearchSummary from RefSeq
DNmechanismLOEUF 1.03
Clinical SummaryCDR2
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
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Clinical Trials
2 active or recruiting trials — potential therapeutic options may be available

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.03LOEUF
pLI 0.000
Z-score 1.48
OE 0.65 (0.421.03)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.85Z-score
OE missense 0.85 (0.760.95)
210 obs / 247.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.65 (0.421.03)
00.351.4
Missense OE0.85 (0.760.95)
00.61.4
Synonymous OE1.19
01.21.6
LoF obs/exp: 13 / 20.2Missense obs/exp: 210 / 247.8Syn Z: -1.52
DN
0.7327th %ile
GOF
0.6151th %ile
LOF
0.3549th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CDR2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold
Clinical Literature
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