CDK16

Chr X

cyclin dependent kinase 16

This X-linked serine/threonine protein kinase regulates vesicle-mediated transport, exocytosis, neuron differentiation, and insulin secretion, with particular roles in growth hormone release and spermatogenesis. Mutations cause X-linked intellectual disability with variable features that may include metabolic dysfunction and developmental delays. The gene is highly constrained against loss-of-function variants, indicating that such mutations are likely to cause significant clinical phenotypes.

OMIMResearchSummary from RefSeq, UniProt
LOFmechanismLOEUF 0.26
Clinical SummaryCDK16
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Gene-Disease Validity (ClinGen)
X-linked complex neurodevelopmental disorder · XLLimited

Limited evidence — not for standalone diagnostic reporting

Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 0.99). One damaged copy is likely sufficient to cause disease.
Some data sources returned errors (1)

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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint
0.26LOEUF
pLI 0.995
Z-score 4.20
OE 0.08 (0.030.26)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint
2.91Z-score
OE missense 0.48 (0.420.56)
122 obs / 252.0 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios
LoF OE0.08 (0.030.26)
00.351.4
Missense OE0.48 (0.420.56)
00.61.4
Synonymous OE0.83
01.21.6
LoF obs/exp: 2 / 24.4Missense obs/exp: 122 / 252.0Syn Z: 1.32
Curated Mechanism (G2P)Gene2Phenotype (DDG2P) ↗
limitedCDK16-related intellectual disabilityLOFmonoallelic_X_heterozygous
DN
0.4289th %ile
GOF
0.4973th %ile
LOF
0.72top 10%

The highest-scoring mechanism for this gene is loss-of-function (haploinsufficiency).

LOFprediction above median · LOEUF 0.26

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312. Mechanism ranking also informed by gnomAD constraint, ClinVar, and ClinGen data.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CDK16 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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