CDCA7L

Chr 7

cell division cycle associated 7 like

Also known as: JPO2, R1, RAM2

CDCA7L encodes a transcriptional repressor that regulates cell proliferation and apoptotic signaling pathways, including inhibition of monoamine oxidase A gene expression. Mutations in this gene cause a neurodevelopmental disorder with intellectual disability and distinctive facial features, inherited in an autosomal recessive pattern. The gene shows low constraint against loss-of-function variants, consistent with recessive inheritance where heterozygous carriers are typically unaffected.

OMIMResearchSummary from RefSeq, UniProt
DNmechanismLOEUF 0.68
Clinical SummaryCDCA7L
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.68LOEUF
pLI 0.000
Z-score 2.85
OE 0.41 (0.260.68)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
-0.09Z-score
OE missense 1.02 (0.921.12)
275 obs / 270.9 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.41 (0.260.68)
00.351.4
Missense OE1.02 (0.921.12)
00.61.4
Synonymous OE1.30
01.21.6
LoF obs/exp: 11 / 27.0Missense obs/exp: 275 / 270.9Syn Z: -2.30
DN
0.6840th %ile
GOF
0.4776th %ile
LOF
0.3648th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CDCA7L · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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