CDC26

Chr 9

cell division cycle 26

Also known as: ANAPC12, APC12, C9orf17

The protein is a component of the anaphase promoting complex/cyclosome (APC/C), an E3 ubiquitin ligase that controls cell cycle progression through mitosis and G1 phase by mediating ubiquitination and degradation of target proteins. Mutations in CDC26 cause autosomal recessive microcephaly and chorioretinopathy, a neurodevelopmental disorder affecting brain growth and retinal development. The gene shows moderate constraint against loss-of-function variants (LOEUF 0.85), consistent with its essential role in cell cycle regulation.

OMIMResearchSummary from RefSeq, UniProt
GOFmechanismLOEUF 0.85
Clinical SummaryCDC26
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.66) — some intolerance to loss-of-function variants.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.85LOEUF
pLI 0.660
Z-score 1.73
OE 0.00 (0.000.85)
Moderately constrained

Typical tolerance to LoF variation

Missense Constraint
0.73Z-score
OE missense 0.71 (0.540.94)
36 obs / 50.7 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.00 (0.000.85)
00.351.4
Missense OE0.71 (0.540.94)
00.61.4
Synonymous OE0.39
01.21.6
LoF obs/exp: 0 / 3.5Missense obs/exp: 36 / 50.7Syn Z: 1.89
DN
0.5279th %ile
GOF
0.79top 25%
LOF
0.49top 25%

The highest-scoring mechanism for this gene is gain-of-function.

GOFprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CDC26 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →