CDC20

Chr 1AR

cell division cycle 20

Also known as: CDC20A, OOMD14, OZEMA14, bA276H19.3, p55CDC

CDC20 encodes a substrate-specific adapter protein for the anaphase promoting complex that targets specific proteins for degradation during the metaphase/anaphase transition of the cell cycle and regulates synaptic vesicle clustering in neurons. Biallelic mutations cause autosomal recessive oocyte/zygote/embryo maturation arrest, resulting in female infertility due to early developmental arrest. The gene shows low constraint to loss-of-function variants (pLI near zero), consistent with the recessive inheritance pattern.

OMIMResearchSummary from RefSeq, OMIM, UniProt
DNmechanismARLOEUF 0.841 OMIM phenotype
Clinical SummaryCDC20
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
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Clinical Trials
1 active or recruiting trial — potential therapeutic options may be available

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.84LOEUF
pLI 0.000
Z-score 2.22
OE 0.54 (0.360.84)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
1.83Z-score
OE missense 0.70 (0.630.79)
208 obs / 296.7 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.54 (0.360.84)
00.351.4
Missense OE0.70 (0.630.79)
00.61.4
Synonymous OE0.86
01.21.6
LoF obs/exp: 15 / 27.6Missense obs/exp: 208 / 296.7Syn Z: 1.14
DN
0.6938th %ile
GOF
0.3094th %ile
LOF
0.50top 25%

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CDC20 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold
Clinical Literature
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