CDC16

Chr 13

cell division cycle 16

Also known as: ANAPC6, APC6, CDC16Hs, CUT9

CDC16 encodes a component of the anaphase promoting complex/cyclosome (APC/C), an E3 ubiquitin ligase that controls cell cycle progression through mitosis and G1 phase by targeting proteins for degradation. Mutations cause autosomal recessive primary microcephaly with seizures and intellectual disability, typically presenting in infancy. The gene is highly constrained against loss-of-function variants (LOEUF 0.379), reflecting its essential role in cell division.

GeneReviewsOMIMResearchSummary from RefSeq, UniProt
LOEUF 0.38
Clinical SummaryCDC16
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.61) — some intolerance to loss-of-function variants.
📋
ClinVar Variants
118 unique Pathogenic / Likely Pathogenic· 88 VUS of 246 total submissions
📖
GeneReview available — CDC16
Authoritative clinical overview · Recommended first read
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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.38LOEUF
pLI 0.614
Z-score 4.52
OE 0.21 (0.120.38)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
1.73Z-score
OE missense 0.73 (0.660.81)
243 obs / 331.5 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.21 (0.120.38)
00.351.4
Missense OE0.73 (0.660.81)
00.61.4
Synonymous OE1.00
01.21.6
LoF obs/exp: 8 / 38.1Missense obs/exp: 243 / 331.5Syn Z: 0.01

ClinVar Variant Classifications

246 submitted variants in ClinVar

Classification Summary

Pathogenic115
Likely Pathogenic3
VUS88
Likely Benign7
Benign3
115
Pathogenic
3
Likely Pathogenic
88
VUS
7
Likely Benign
3
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
115
0
115
Likely Pathogenic
0
0
3
0
3
VUS
0
71
17
0
88
Likely Benign
0
2
4
1
7
Benign
0
0
2
1
3
Total0731412216

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

CDC16 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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