CDADC1

Chr 13

cytidine and dCMP deaminase domain containing 1

Also known as: NYD-SP15, bA103J18.1

The protein catalyzes the deamination of cytidine and deoxycytidine into uridine and deoxyuridine, respectively, and may play an important role in testicular development and spermatogenesis. Mutations cause autosomal recessive primary immunodeficiency with defective lymphocyte apoptosis and autoimmunity. This gene is extremely intolerant to loss-of-function variants, suggesting complete loss of protein function is likely incompatible with normal development.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
3
Pubs (1 yr)
61
P/LP submissions
0%
P/LP missense
1.10
LOEUF
Mechanism
Clinical SummaryCDADC1
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
61 unique Pathogenic / Likely Pathogenic· 46 VUS of 126 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.10LOEUF
pLI 0.000
Z-score 1.18
OE 0.74 (0.511.10)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
1.47Z-score
OE missense 0.75 (0.670.84)
202 obs / 270.1 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.74 (0.511.10)
00.351.4
Missense OE0.75 (0.670.84)
00.61.4
Synonymous OE0.93
01.21.6
LoF obs/exp: 18 / 24.3Missense obs/exp: 202 / 270.1Syn Z: 0.57

ClinVar Variant Classifications

126 submitted variants in ClinVar

Classification Summary

Pathogenic59
Likely Pathogenic2
VUS46
Likely Benign4
59
Pathogenic
2
Likely Pathogenic
46
VUS
4
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
59
0
59
Likely Pathogenic
0
0
2
0
2
VUS
0
41
5
0
46
Likely Benign
0
3
0
1
4
Benign
0
0
0
0
0
Total044661111

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

CDADC1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC