CD59

Chr 11

CD59 molecule (CD59 blood group)

Also known as: 16.3A5, 1F5, EJ16, EJ30, EL32, G344, HRF-20, HRF20

This gene encodes a cell surface glycoprotein that regulates complement-mediated cell lysis, and it is involved in lymphocyte signal transduction. This protein is a potent inhibitor of the complement membrane attack complex, whereby it binds complement C8 and/or C9 during the assembly of this complex, thereby inhibiting the incorporation of multiple copies of C9 into the complex, which is necessary for osmolytic pore formation. This protein also plays a role in signal transduction pathways in the activation of T cells. Mutations in this gene cause CD59 deficiency, a disease resulting in hemolytic anemia and thrombosis, and which causes cerebral infarction. Multiple alternatively spliced transcript variants, which encode the same protein, have been identified for this gene. [provided by RefSeq, Jul 2008]

GeneReviewsResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtHemolytic anemia, CD59-mediated, with or without polyneuropathy

Clinical highlights

Interpreting a novel variant
This gene is strongly intolerant of loss-of-function variation in the population, so LoF variants warrant close attention. No curated mechanism annotation is available — see the mechanism card for the computational prediction and its caveats.Based on population constraint only.
1
Active trials
133
Pubs (1 yr)
P/LP submissions
P/LP missense
1.00
LOEUF
DN
Mechanism· predicted
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GeneReview available — CD59
Authoritative clinical overview · Recommended first read
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Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint?
1.00LOEUF
pLI 0.606
Z-score 1.59
OE 0.00 (0.001.00)
Moderately constrained

Highly tolerant — LoF variants common in population

Missense Constraint?
-0.05Z-score
OE missense 1.02 (0.831.25)
67 obs / 66.0 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?0.00 (0.001.00)
00.351.4
Missense OE?1.02 (0.831.25)
00.61.4
Synonymous OE?1.07
01.21.6
LoF obs/exp: 0 / 2.9Missense obs/exp: 67 / 66.0Syn Z: -0.29

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CD59 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.