CD52

Chr 1

CD52 molecule

Also known as: CDW52, EDDM5, HE5

The CD52 protein is involved in positive regulation of cytosolic calcium ion concentration and is located in the extracellular region and plasma membrane. Mutations in CD52 cause immunodeficiency disorders with autosomal recessive inheritance. The gene shows moderate tolerance to loss-of-function variants, and a GeneReviews entry is available for detailed clinical information.

GeneReviewsOMIMResearchSummary from RefSeq, UniProt
MultiplemechanismLOEUF 1.70
Clinical SummaryCD52
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.00) despite low pLI — interpret in context.
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Clinical Trials
1 active or recruiting trial — potential therapeutic options may be available
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GeneReview available — CD52
Authoritative clinical overview · Recommended first read
Open GeneReview ↗

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.70LOEUF
pLI 0.403
Z-score 0.96
OE 0.00 (0.001.70)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.51Z-score
OE missense 0.76 (0.561.05)
27 obs / 35.6 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.00 (0.001.70)
00.351.4
Missense OE0.76 (0.561.05)
00.61.4
Synonymous OE0.80
01.21.6
LoF obs/exp: 0 / 1.1Missense obs/exp: 27 / 35.6Syn Z: 0.60
DN
0.7230th %ile
GOF
0.79top 10%
LOF
0.1895th %ile

This gene has evidence for multiple mechanisms of pathogenicity (gain-of-function and dominant-negative). Both the Badonyi & Marsh prediction and the broader genomic evidence point to gain-of-function as the predominant mechanism. Different variants in this gene may act through different mechanisms — interpret in context of the specific variant.

GOFprediction above median
DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CD52 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold
Clinical Literature
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Full-Text Mentions
NLP-detected gene mentions in article bodies · via PubTator3
PubTator3
Top 5 full-text resultsSearch PubTator3 ↗