CD247

Chr 1AR

CD247 molecule

Also known as: CD3-ZETA, CD3H, CD3Q, CD3Z, CD3ZETA, IMD25, T3Z, TCRZ

The protein encoded by this gene is T-cell receptor zeta, which together with T-cell receptor alpha/beta and gamma/delta heterodimers, and with CD3-gamma, -delta and -epsilon, forms the T-cell receptor-CD3 complex. The zeta chain plays an important role in coupling antigen recognition to several intracellular signal-transduction pathways. Low expression of the antigen results in impaired immune response. Two alternatively spliced transcript variants encoding distinct isoforms have been found for this gene. [provided by RefSeq, Jul 2008]

OMIMResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

?Immunodeficiency 25MIM #610163
AR

Clinical highlights

Gene-disease validity (ClinGen)
immunodeficiency 25 · ARDefinitivesufficient evidence for diagnostic panels
0
Active trials
38
Pubs (1 yr)
P/LP submissions
P/LP missense
0.82
LOEUF
Multiple*
Mechanism· predicted

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.82LOEUF
pLI 0.017
Z-score 2.01
OE 0.39 (0.200.82)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
-0.31Z-score
OE missense 1.09 (0.931.28)
104 obs / 95.5 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?0.39 (0.200.82)
00.351.4
Missense OE?1.09 (0.931.28)
00.61.4
Synonymous OE?0.87
01.21.6
LoF obs/exp: 5 / 12.8Missense obs/exp: 104 / 95.5Syn Z: 0.65

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CD247 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →