CD200R1L

Chr 3

CD200 receptor 1 like

Also known as: CD200R2, CD200RLa

CD200R1L encodes a predicted signaling receptor that may function as a receptor for the CD200/OX2 cell surface glycoprotein and is involved in regulation of neuroinflammatory responses. The gene shows low constraint against loss-of-function variants (LOEUF 0.936), and no definitive human disease associations have been established for pathogenic variants in this gene. Clinical significance of CD200R1L variants in pediatric neurological conditions remains to be determined.

ResearchSummary from RefSeq, UniProt
MultiplemechanismLOEUF 0.94
Clinical SummaryCD200R1L
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.94LOEUF
pLI 0.003
Z-score 1.73
OE 0.47 (0.260.94)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
-0.41Z-score
OE missense 1.10 (0.961.25)
160 obs / 145.9 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.47 (0.260.94)
00.351.4
Missense OE1.10 (0.961.25)
00.61.4
Synonymous OE1.32
01.21.6
LoF obs/exp: 6 / 12.6Missense obs/exp: 160 / 145.9Syn Z: -1.86
DN
0.7326th %ile
GOF
0.7127th %ile
LOF
0.2580th %ile

This gene has evidence for multiple mechanisms of pathogenicity (dominant-negative and gain-of-function). Both the Badonyi & Marsh prediction and the broader genomic evidence point to dominant-negative as the predominant mechanism. Different variants in this gene may act through different mechanisms — interpret in context of the specific variant.

DNprediction above median
GOFprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CD200R1L · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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