CD200

Chr 3

CD200 molecule

Also known as: MOX1, MOX2, MRC, OX-2

The CD200 protein is a type I membrane glycoprotein that costimulates T-cell proliferation and regulates myeloid cell activity across various tissues. Mutations cause early-onset immunodeficiency with recurrent infections, growth retardation, and developmental delays with autosomal recessive inheritance. The gene is highly constrained against loss-of-function variants (LOEUF 0.56), indicating that complete loss of function is likely pathogenic.

OMIMResearchSummary from RefSeq, UniProt
DNmechanismLOEUF 0.56
Clinical SummaryCD200
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.22) despite low pLI — interpret in context.
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Clinical Trials
1 active or recruiting trial — potential therapeutic options may be available

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.56LOEUF
pLI 0.414
Z-score 2.70
OE 0.22 (0.100.56)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
0.66Z-score
OE missense 0.85 (0.740.98)
138 obs / 161.4 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.22 (0.100.56)
00.351.4
Missense OE0.85 (0.740.98)
00.61.4
Synonymous OE1.01
01.21.6
LoF obs/exp: 3 / 13.9Missense obs/exp: 138 / 161.4Syn Z: -0.08
DN
0.6455th %ile
GOF
0.6053th %ile
LOF
0.3550th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CD200 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold
Clinical Literature
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