CCT5

Chr 5AR

chaperonin containing TCP1 subunit 5

Also known as: CCT-epsilon, CCTE, HEL-S-69, HSNSP, PNAS-102, TCP-1-epsilon

The CCT5 protein is a component of the chaperonin-containing T-complex (TRiC) that assists in folding actin, tubulin, and other proteins in an ATP-dependent manner. Mutations cause hereditary sensory neuropathy with spastic paraplegia, inherited in an autosomal recessive pattern. This gene is highly constrained against loss-of-function variants, indicating it is essential for normal cellular function.

OMIMResearchSummary from RefSeq, OMIM, UniProt
LOFmechanismARLOEUF 0.191 OMIM phenotype
Clinical SummaryCCT5
Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 1.00). One damaged copy is likely sufficient to cause disease.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint
0.19LOEUF
pLI 0.999
Z-score 4.48
OE 0.04 (0.010.19)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint
1.47Z-score
OE missense 0.77 (0.690.85)
239 obs / 312.4 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.04 (0.010.19)
00.351.4
Missense OE0.77 (0.690.85)
00.61.4
Synonymous OE1.06
01.21.6
LoF obs/exp: 1 / 25.3Missense obs/exp: 239 / 312.4Syn Z: -0.49
Curated Mechanism (G2P)Gene2Phenotype (DDG2P) ↗
limitedCCT5-related neurodevelopmental disorder with brain abnormalitiesLOFAD
DN
0.4487th %ile
GOF
0.4184th %ile
LOF
0.64top 25%

The highest-scoring mechanism for this gene is loss-of-function (haploinsufficiency).

LOFprediction above median · LOEUF 0.19

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312. Mechanism ranking also informed by gnomAD constraint, ClinVar, and ClinGen data.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CCT5 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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