CCT3

Chr 1AD

chaperonin containing TCP1 subunit 3

Also known as: CCT-gamma, CCTG, NEDSVH, PIG48, TCP-1-gamma, TRIC5

CCT3 encodes a component of the chaperonin-containing T-complex (TRiC), a molecular chaperone that assists ATP-dependent folding of actin, tubulin, and other proteins essential for cellular function. Mutations cause autosomal dominant neurodevelopmental disorder with speech or visual impairment and brain hypomyelination. The gene is highly constrained against loss-of-function variants (pLI 1.0, LOEUF 0.097), indicating intolerance to protein disruption.

OMIMResearchSummary from RefSeq, OMIM, UniProt
LOFmechanismADLOEUF 0.101 OMIM phenotype
Clinical SummaryCCT3
Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 1.00). One damaged copy is likely sufficient to cause disease.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint
0.10LOEUF
pLI 1.000
Z-score 5.13
OE 0.00 (0.000.10)
Highly constrained

Among the most LoF-intolerant genes (~top 3%)

Missense Constraint
1.16Z-score
OE missense 0.82 (0.740.91)
276 obs / 335.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.00 (0.000.10)
00.351.4
Missense OE0.82 (0.740.91)
00.61.4
Synonymous OE0.94
01.21.6
LoF obs/exp: 0 / 30.7Missense obs/exp: 276 / 335.8Syn Z: 0.46
Curated Mechanism (G2P)Gene2Phenotype (DDG2P) ↗
moderateCCT3-related neurodevelopmental disorder with hypomyelination of white matterLOFAD
DN
0.3991th %ile
GOF
0.3690th %ile
LOF
0.68top 10%

The highest-scoring mechanism for this gene is loss-of-function (haploinsufficiency).

LOFprediction above median · LOEUF 0.10

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312. Mechanism ranking also informed by gnomAD constraint, ClinVar, and ClinGen data.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CCT3 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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