CCSER1

Chr 4

coiled-coil serine rich protein 1

Also known as: FAM190A

The CCSER1 protein function remains poorly characterized, with limited clinical data available beyond an association with cocaine dependence. This gene is not well-constrained against loss-of-function variants (pLI = 0.0008, LOEUF = 0.55), and no established pediatric neurogenetic disorders have been definitively linked to CCSER1 mutations in the medical literature.

Summary from RefSeq
Research Assistant →
0
Active trials
5
Pubs (1 yr)
0
P/LP submissions
P/LP missense
0.55
LOEUF
DN
Mechanism· predicted
Clinical SummaryCCSER1
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.34) despite low pLI — interpret in context.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.55LOEUF
pLI 0.001
Z-score 3.64
OE 0.34 (0.220.55)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
1.12Z-score
OE missense 0.85 (0.790.93)
397 obs / 464.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.34 (0.220.55)
00.351.4
Missense OE0.85 (0.790.93)
00.61.4
Synonymous OE0.97
01.21.6
LoF obs/exp: 12 / 35.4Missense obs/exp: 397 / 464.8Syn Z: 0.29
DN
0.6453th %ile
GOF
0.5367th %ile
LOF
0.50top 25%

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CCSER1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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