CCDC80

Chr 3

coiled-coil domain containing 80

Also known as: CL2, DRO1, LINC01279, SSG1, URB, okuribin

The CCDC80 protein promotes cell adhesion and matrix assembly through fibronectin and heparin binding activities in the extracellular matrix. Mutations cause autosomal recessive intellectual disability with short stature and behavioral abnormalities. The gene shows moderate constraint against loss-of-function variants (LOEUF 0.65).

OMIMResearchSummary from RefSeq, UniProt
LOEUF 0.65
Clinical SummaryCCDC80
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.65LOEUF
pLI 0.000
Z-score 3.19
OE 0.42 (0.280.65)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
0.44Z-score
OE missense 0.95 (0.881.02)
522 obs / 551.1 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.42 (0.280.65)
00.351.4
Missense OE0.95 (0.881.02)
00.61.4
Synonymous OE1.03
01.21.6
LoF obs/exp: 15 / 35.5Missense obs/exp: 522 / 551.1Syn Z: -0.30

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CCDC80 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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