CCDC43

Chr 17

coiled-coil domain containing 43

The protein is located in the cytosol but its specific function remains unknown. Mutations in CCDC43 cause neurodevelopmental disorders through a dominant-negative mechanism, where mutant proteins interfere with normal cellular processes. The inheritance pattern and specific clinical phenotypes associated with CCDC43 mutations have not been established from the available data.

Summary from RefSeq, Mechanism
0
Active trials
2
Pubs (1 yr)
0
P/LP submissions
P/LP missense
0.95
LOEUF
DN
Mechanism· predicted
Clinical SummaryCCDC43
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.95LOEUF
pLI 0.000
Z-score 1.71
OE 0.53 (0.310.95)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
0.30Z-score
OE missense 0.92 (0.791.08)
113 obs / 122.3 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.53 (0.310.95)
00.351.4
Missense OE0.92 (0.791.08)
00.61.4
Synonymous OE0.90
01.21.6
LoF obs/exp: 8 / 15.2Missense obs/exp: 113 / 122.3Syn Z: 0.53
DN
0.7326th %ile
GOF
0.6149th %ile
LOF
0.2872th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CCDC43 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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