CCDC107

Chr 9

coiled-coil domain containing 107

Also known as: PSEC0222

The protein is a membrane protein containing a coiled-coil domain with multiple isoforms produced through alternative splicing. Mutations cause autosomal recessive primary ciliary dyskinesia, a disorder affecting ciliary function that leads to chronic respiratory infections, sinusitis, and often situs inversus. Symptoms typically begin in infancy or early childhood with recurrent pneumonia and bronchiectasis.

ResearchSummary from RefSeq
DNmechanismLOEUF 1.72
Clinical SummaryCCDC107
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.72LOEUF
pLI 0.000
Z-score -0.29
OE 1.09 (0.701.72)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.19Z-score
OE missense 0.95 (0.831.10)
139 obs / 145.6 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE1.09 (0.701.72)
00.351.4
Missense OE0.95 (0.831.10)
00.61.4
Synonymous OE0.96
01.21.6
LoF obs/exp: 12 / 11.0Missense obs/exp: 139 / 145.6Syn Z: 0.25
DN
0.6454th %ile
GOF
0.5661th %ile
LOF
0.3744th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CCDC107 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC