CAV3

Chr 3

caveolin 3

Also known as: LGMD1C, LQT9, MPDT, RMD2, VIP-21, VIP21

This gene encodes a caveolin family member, which functions as a component of the caveolae plasma membranes found in most cell types. Caveolin proteins are proposed to be scaffolding proteins for organizing and concentrating certain caveolin-interacting molecules. Mutations identified in this gene lead to interference with protein oligomerization or intra-cellular routing, disrupting caveolae formation and resulting in Limb-Girdle muscular dystrophy type-1C (LGMD-1C), hyperCKemia or rippling muscle disease (RMD). Alternative splicing has been identified for this locus, with inclusion or exclusion of a differentially spliced intron. In addition, transcripts utilize multiple polyA sites and contain two potential translation initiation sites. [provided by RefSeq, Jul 2008]

GeneReviewsResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtHyperCKmia
UniProtRippling muscle disease 2
UniProtCardiomyopathy, familial hypertrophic
UniProtLong QT syndrome 9

Clinical highlights

Gene-disease validity (ClinGen)
long QT syndrome · ADLimitednot for standalone diagnostic reporting2 gene-disease associations curated in total
0
Active trials
29
Pubs (1 yr)
P/LP submissions
P/LP missense
1.47
LOEUF
Multiple*
Mechanism· predicted
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GeneReview available — CAV3
Authoritative clinical overview · Recommended first read
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Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.47LOEUF
pLI 0.005
Z-score 0.79
OE 0.66 (0.321.47)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
0.83Z-score
OE missense 0.76 (0.620.92)
69 obs / 91.3 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.66 (0.321.47)
00.351.4
Missense OE?0.76 (0.620.92)
00.61.4
Synonymous OE?1.12
01.21.6
LoF obs/exp: 4 / 6.1Missense obs/exp: 69 / 91.3Syn Z: -0.58

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CAV3 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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