This gene encodes catalase, a key antioxidant enzyme in the bodies defense against oxidative stress. Catalase is a heme enzyme that is present in the peroxisome of nearly all aerobic cells. Catalase converts the reactive oxygen species hydrogen peroxide to water and oxygen and thereby mitigates the toxic effects of hydrogen peroxide. Oxidative stress is hypothesized to play a role in the development of many chronic or late-onset diseases such as diabetes, asthma, Alzheimer's disease, systemic lupus erythematosus, rheumatoid arthritis, and cancers. Polymorphisms in this gene have been associated with decreases in catalase activity but, to date, acatalasemia is the only disease known to be caused by this gene. [provided by RefSeq, Oct 2009]

GeneReviewsResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtAcatalasemia

Clinical highlights

Gene-disease validity (ClinGen)
acatalasia · ARModerateconsider for supplementary testing
12
Active trials
13088
Pubs (1 yr)
P/LP submissions
P/LP missense
1.05
LOEUF
DN
Mechanism· predicted
📖
GeneReview available — CAT
Authoritative clinical overview · Recommended first read
Open GeneReview ↗
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.05LOEUF
pLI 0.000
Z-score 1.34
OE 0.72 (0.501.05)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
-0.08Z-score
OE missense 1.01 (0.921.11)
316 obs / 312.1 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?0.72 (0.501.05)
00.351.4
Missense OE?1.01 (0.921.11)
00.61.4
Synonymous OE?1.04
01.21.6
LoF obs/exp: 19 / 26.4Missense obs/exp: 316 / 312.1Syn Z: -0.35

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CAT · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

Advanced Bladder CarcinomaAdvanced Genitourinary System CarcinomaMetastatic Bladder Carcinoma

Testing Olaparib in Patients With Advanced or Metastatic (Cancer That Has Spread) Bladder Cancer and Other Genitourinary Tumors With DNA-Repair Genetic Changes

ACTIVE NOT RECRUITING
NCT03375307Phase PHASE2National Cancer Institute (NCI)Started 2020-11-03
Biopsy ProcedureBiospecimen CollectionBone Marrow Biopsy
Bleeding Disorder

Early Genomic Testing for Inherited Bleeding Disorders

RECRUITING
NCT06736158Phase EARLY_PHASE1Queen's UniversityStarted 2025-05-31
Genetic testing for inherited bleeding disorders
Advanced Malignant Solid NeoplasmMetastatic Malignant Solid Neoplasm

Personalized Antibody-Drug Conjugate Therapy Based on RNA and Protein Testing for the Treatment of Advanced or Metastatic Solid Tumors (The ADC MATCH Screening and Treatment Trial)

RECRUITING
NCT06311214Phase PHASE2National Cancer Institute (NCI)Started 2025-03-18
Biopsy ProcedureBiospecimen CollectionComputed Tomography
Insulin SensitivityOverweight or ObesityInflammatory Response

Pulses Consumption and Its Role in Managing Systemic Inflammation, Insulin Sensitivity and Gut Microbiome in Human

ACTIVE NOT RECRUITING
NCT04267705Phase NAClinical Nutrition Research Center, Illinois Institute of TechnologyStarted 2020-02-24
ControlBlack beanChickpea
Advanced Pancreatic CarcinomaMetastatic Pancreatic CarcinomaStage II Pancreatic Cancer AJCC v8

A Phase II Nationwide, Fully Decentralized, Telemedicine Study of Pemigatinib in Adult Patients With Advanced or Metastatic Pancreatic Cancer With FGFR Genetic Alterations

RECRUITING
NCT06906562Phase PHASE2Sameek RoychowdhuryStarted 2025-08-26
PemigatinibComputed Tomography (CT)Magnetic Resonance Imaging
Hemophilia A

Study to Evaluate the Efficacy and Safety of PF-07055480 / Giroctocogene Fitelparvovec Gene Therapy in Moderately Severe to Severe Hemophilia A Adults

ACTIVE NOT RECRUITING
NCT04370054Phase PHASE3PfizerStarted 2020-08-18
PF-07055480 (giroctocogene fitelparovec): Recombinant AAV2/6 Human Factor VIII Gene Therapy
Microbiome AnalysisDrug Abuse in PregnancyAlcohol Abuse in Pregnancy

Alcohol and Cannabis Use Among Pregnant Slovenian Women

ENROLLING BY INVITATION
NCT07456579University Medical Centre LjubljanaStarted 2024-05-05
Anatomic Stage IV Breast Cancer AJCC v8Hormone Receptor Positive Breast CarcinomaMetastatic Breast Carcinoma

Using FDG-PET/CT to Assess Response of Bone-Dominant Metastatic Breast Cancer, FEATURE Study

ACTIVE NOT RECRUITING
NCT04316117Phase PHASE2ECOG-ACRIN Cancer Research GroupStarted 2020-09-15
Computed TomographyFludeoxyglucose F-18Positron Emission Tomography
Myeloproliferative Neoplasms

Registry of Patients With MPNs in Taiwan

ACTIVE NOT RECRUITING
NCT03618485Chang Gung Memorial HospitalStarted 2017-04-01
Prediabetes

Effect of Increased Physical Activity and Stopping Evening Snacking in Metabolic Health in Youth With Prediabetes

RECRUITING
NCT06782906Phase NABaylor College of MedicineStarted 2025-05-13
≥10,000 daily steps (≥5 days/week) and stopping evening snacking
Rare Malignant NeoplasmAdvanced Solid TumorsMetastatic Solid Tumors

Rare Tumor Focused Platform Study of Innovative Therapies and Technologies (PLATFORM2)

NOT YET RECRUITING
NCT07307053Phase PHASE1, PHASE2Cancer Institute and Hospital, Chinese Academy of Medical SciencesStarted 2026-01-01
BL-B01D1VSV injectionCVL006
Fallopian Tube CarcinomaFallopian Tube Endometrioid AdenocarcinomaFallopian Tube Serous Adenocarcinoma

Testing the Combination of the Study Drugs Cediranib and Olaparib in Recurrent Ovarian Cancer

ACTIVE NOT RECRUITING
NCT02345265Phase PHASE2National Cancer Institute (NCI)Started 2016-05-23
Biopsy ProcedureBiospecimen CollectionCediranib Maleate