CARNMT1

Chr 9

carnosine N-methyltransferase 1

Also known as: C9orf41, UPF0586

The protein encoded by this gene is a methyltransferase that converts carnosine to anserine and methylates other histidine-containing dipeptides and tripeptides. This gene is not well-established as a cause of human disease, with very low constraint against loss-of-function variants suggesting that complete loss of function may be tolerated in humans.

OMIMResearchSummary from RefSeq, UniProt
LOEUF 0.69
Clinical SummaryCARNMT1
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
39 unique Pathogenic / Likely Pathogenic· 55 VUS of 104 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.69LOEUF
pLI 0.002
Z-score 2.60
OE 0.39 (0.230.69)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
1.88Z-score
OE missense 0.63 (0.550.73)
130 obs / 205.7 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.39 (0.230.69)
00.351.4
Missense OE0.63 (0.550.73)
00.61.4
Synonymous OE1.00
01.21.6
LoF obs/exp: 8 / 20.8Missense obs/exp: 130 / 205.7Syn Z: 0.01

ClinVar Variant Classifications

104 submitted variants in ClinVar

Classification Summary

Pathogenic34
Likely Pathogenic5
VUS55
Likely Benign1
Benign1
34
Pathogenic
5
Likely Pathogenic
55
VUS
1
Likely Benign
1
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
34
0
34
Likely Pathogenic
0
1
4
0
5
VUS
0
48
7
0
55
Likely Benign
0
0
0
1
1
Benign
0
0
0
1
1
Total04945296

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

CARNMT1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Full-Text Mentions
NLP-detected gene mentions in article bodies · via PubTator3
PubTator3
Top 5 full-text resultsSearch PubTator3 ↗
Key Publications
Landmark & review papers · by relevance
PubMed
Top 1 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC