CAPRIN2

Chr 12

caprin family member 2

Also known as: C1QDC1, EEG-1, EEG1, RNG140

CAPRIN2 encodes a protein that regulates mRNA transport and translation, promotes Wnt signaling pathway activity through LRP6 phosphorylation, and is involved in erythroblast differentiation. Mutations cause autosomal recessive developmental and epileptic encephalopathy with movement abnormalities, presenting in early infancy with severe intellectual disability, seizures, and dystonic movements. The gene shows high constraint against loss-of-function variants (LOEUF 0.38), indicating intolerance to protein-truncating mutations.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
5
Pubs (1 yr)
32
P/LP submissions
0%
P/LP missense
0.38
LOEUF
Mechanism
Clinical SummaryCAPRIN2
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.24) despite low pLI — interpret in context.
📋
ClinVar Variants
32 unique Pathogenic / Likely Pathogenic· 135 VUS of 209 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.38LOEUF
pLI 0.102
Z-score 5.31
OE 0.24 (0.160.38)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
0.61Z-score
OE missense 0.93 (0.861.00)
504 obs / 544.3 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.24 (0.160.38)
00.351.4
Missense OE0.93 (0.861.00)
00.61.4
Synonymous OE1.04
01.21.6
LoF obs/exp: 14 / 57.5Missense obs/exp: 504 / 544.3Syn Z: -0.47

ClinVar Variant Classifications

209 submitted variants in ClinVar

Classification Summary

Pathogenic29
Likely Pathogenic3
VUS135
Likely Benign6
Benign6
29
Pathogenic
3
Likely Pathogenic
135
VUS
6
Likely Benign
6
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
29
0
29
Likely Pathogenic
0
0
3
0
3
VUS
1
133
1
0
135
Likely Benign
0
5
0
1
6
Benign
0
1
2
3
6
Total1139354179

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

CAPRIN2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 1 results · since 2015Search PubMed ↗