CAPN7

Chr 3

calpain 7

Also known as: CALPAIN7, PALBH

CAPN7 encodes a calcium-regulated cysteine protease that cleaves proteins in a non-lysosomal cellular compartment. Mutations cause autosomal recessive spastic paraplegia with microcephaly and intellectual disability, typically presenting in early childhood. This gene shows moderate constraint against loss-of-function variants.

OMIMResearchSummary from RefSeq, UniProt
LOEUF 0.79
Clinical SummaryCAPN7
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
23 unique Pathogenic / Likely Pathogenic· 89 VUS of 140 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.79LOEUF
pLI 0.000
Z-score 2.76
OE 0.58 (0.430.79)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
1.21Z-score
OE missense 0.83 (0.760.91)
347 obs / 416.7 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.58 (0.430.79)
00.351.4
Missense OE0.83 (0.760.91)
00.61.4
Synonymous OE1.10
01.21.6
LoF obs/exp: 29 / 50.1Missense obs/exp: 347 / 416.7Syn Z: -0.90

ClinVar Variant Classifications

140 submitted variants in ClinVar

Classification Summary

Pathogenic22
Likely Pathogenic1
VUS89
Likely Benign7
22
Pathogenic
1
Likely Pathogenic
89
VUS
7
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
22
0
22
Likely Pathogenic
0
0
1
0
1
VUS
2
85
2
0
89
Likely Benign
0
6
0
1
7
Benign
0
0
0
0
0
Total291251119

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

CAPN7 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 2 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC