CANT1

Chr 17AR

calcium activated nucleotidase 1

Also known as: DBQD, DBQD1, EDM7, SCAN-1, SCAN1, SHAPY

This protein encoded by this gene belongs to the apyrase family. It functions as a calcium-dependent nucleotidase with a preference for UDP. Mutations in this gene are associated with Desbuquois dysplasia with hand anomalies. Alternatively spliced transcript variants have been noted for this gene.[provided by RefSeq, Mar 2010]

GeneReviewsOMIMResearchGenerating clinical summary…
LOFmechanismARLOEUF 1.312 OMIM phenotypes
Clinical SummaryCANT1
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Gene-Disease Validity (ClinGen)
Desbuquois dysplasia 1 · ARDefinitive

Definitive — sufficient evidence for diagnostic panels

Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
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ClinVar Variants
50 unique Pathogenic / Likely Pathogenic· 159 VUS of 464 total submissions
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GeneReview available — CANT1
Authoritative clinical overview · Recommended first read
Open GeneReview ↗

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.31LOEUF
pLI 0.000
Z-score 0.76
OE 0.77 (0.471.31)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
0.49Z-score
OE missense 0.92 (0.821.02)
243 obs / 265.4 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.77 (0.471.31)
00.351.4
Missense OE?0.92 (0.821.02)
00.61.4
Synonymous OE?0.89
01.21.6
LoF obs/exp: 10 / 13.0Missense obs/exp: 243 / 265.4Syn Z: 0.94

ClinVar Variant Classifications

464 submitted variants in ClinVar

Classification Summary

Pathogenic30
Likely Pathogenic20
VUS159
Likely Benign193
Benign27
Conflicting27
30
Pathogenic
20
Likely Pathogenic
159
VUS
193
Likely Benign
27
Benign
27
Conflicting

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
25
4
1
0
30
Likely Pathogenic
8
11
1
0
20
VUS
2
109
46
2
159
Likely Benign
0
7
40
146
193
Benign
0
0
21
6
27
Conflicting
27
Total35131109154456

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

17 pathogenic / likely-pathogenic (of 29) ClinVar copy-number / structural variants overlap CANT1 — these span large chromosomal regions, not the gene specifically, and are excluded from the counts above. Explore in CNV tools →

Protein Context — Lollipop Plot

CANT1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →