CACNB2

Chr 10

calcium voltage-gated channel auxiliary subunit beta 2

Also known as: CAB2, CACNLB2, CAVB2, MYSB

This gene encodes a subunit of a voltage-dependent calcium channel protein that is a member of the voltage-gated calcium channel superfamily. The gene product was originally identified as an antigen target in Lambert-Eaton myasthenic syndrome, an autoimmune disorder. Mutations in this gene are associated with Brugada syndrome. Alternatively spliced variants encoding different isoforms have been described. [provided by RefSeq, Feb 2013]

GeneReviewsResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtBrugada syndrome 4

Clinical highlights

Gene-disease validity (ClinGen)
cardiogenetic disease · ADDisputedevidence questions this relationship
0
Active trials
20
Pubs (1 yr)
P/LP submissions
P/LP missense
0.69
LOEUF
DN
Mechanism· predicted
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GeneReview available — CACNB2
Authoritative clinical overview · Recommended first read
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Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.69LOEUF
pLI 0.000
Z-score 2.95
OE 0.45 (0.300.69)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
0.07Z-score
OE missense 0.99 (0.911.08)
390 obs / 393.7 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.45 (0.300.69)
00.351.4
Missense OE?0.99 (0.911.08)
00.61.4
Synonymous OE?1.24
01.21.6
LoF obs/exp: 15 / 33.4Missense obs/exp: 390 / 393.7Syn Z: -2.22

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CACNB2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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